Late-onset Hip Dysplasia and Dislocation in Osteogenesis Imperfecta

Abstract

Background: Skeletal deformities and multiple fractures are the most common features of osteogenesis imperfecta which frequently has been managed using intramedullary nails. Likewise, hip dysplasia is considered a rare complication of osteogenesis imperfecta. Hereby we want to describe a patient with osteogenesis imperfecta who developed late-onset hip dysplasia and multiple subluxations.

Case presentation: Here, we presented a 7-year-old girl, known case of osteogenesis imperfecta, who was referred to our clinic for limping and limb length discrepancy. During the radiological assessments, we found increasing acetabular index and mild hip dysplasia as well as coxa valga while the previous radiographs were indicated normal hips. Salter osteotomy was performed to improve the anterior coverage of the left side and Dega osteotomy was performed on the right side to improve anterior and posterior coverages. In further follow up both hips were reduced and acetabular indexes seem normal.

Conclusion: Femoral intramedullary rods insertion can destroy the physis of the greater trochanter which conduce to coxa valga. Hyperlaxity along with valgus deformity led to multiple hip subluxation and dysplasia.